Congenital Adrenal Hyperplasia

A Comprehensive Guide

Peter C. Hindmarsh, Kathy Geertsma, Peter C Hindmarsh

• Publisher: Academic Press
• Year: 2017
• eBook ISBN: 9780128114841
• Topic: Medicine
• Subtopic: Endocrinology & Metabolism

Congenital Adrenal Hyperplasia: A Comprehensive Guide addresses how hydrocortisone works, what can go wrong, and how to correct it, also explaining why the timing of doses and measurement of cortisol from a dose is extremely important.The book provides an in-depth analysis of this disorder for pediatric endocrinologists and primary care providers, allowing them to help patients with an updated model of care and appropriate treatment.Patients and family members will benefit from the trend-forward information that will empower them to approach their healthcare providers with the expectation of receiving individualized care and treatment for this disorder.- Outlines the basics of congenital adrenal hyperplasia and its interrelation with hormones and bodily functions- Presents the known cognitive and emotional aspects of the disease- Reviews multidisciplinary management as well as post-treatment management of the disease

Appendix 1

Converting System International (SI) Blood Measures Into North American Values or Conventional Units

In this book we have used the units of measurement that are used in Europe called the System International (SI). If you are from North America or some other part of the world where this system is not commonly used, then blood results are presented in different units, often referred to as conventional units. To help you understand the graphs better, you can convert the SI measures to the conventional or North American measures using the following table.

Appendix 2

List of Abbreviations

Index

A

Accident, 396–398

Acne vulgaris, 187

ACTH, See Adrenocorticotropin hormone (ACTH)

Addison’s disease, 179, 262

timing of last dose, effect of, 180

Adrenal androgens, 12, 123, 130, 131, 136, 138

backdoor pathway for, formation of, 14

CAH poor control, effect of, 131

DHEA, 15

male hormones, 14

classic pathway for, production, 15, 16

in female, 14

in male, 13

Adrenal cortex, 4, 141

Adrenal crisis, 146, 224, 387

components of, 43, 44

glucogel application, role of, 229

intramuscular hydrocortisone, role of, 229

Adrenalectomy, 419–420

Adrenal gland, 126, 130, 199, 213, 221, 315

blood flow, 221

changes with age, 97

feedback from, adrenal to pituitary, 104

low adrenal androgen, effect of, 162, 164

physiology of, 3

division of, 6

relation with kidney, 4

testosterone production, 16

transverse section of, 7

Adrenal hypoplasia congenital, 262, See also Congenital adrenal hyperplasia (CAH)

Adrenaline, 4, 380

effects, 380, 382

producing cell, 221

Adrenal insufficiency, 405

Adrenal medulla, 4

Adrenal replacement therapy, 210

Adrenal rests, 118, 164–171

Adrenocorticotropin hormone (ACTH), 5, 267

CAH, role in, 309–311

24-h profile in young adult, 310

Advanced bone age, 124–128

Albumin, 213

Aldosterone, 5

control of, sodium chloride, 12

maintaining, blood volume a...

Table of contents

• Cover
• Title page
• Contents
• Copyright
• Personal Story
• A Medical View
• Introduction
• Section One: Congenital adrenal hyperplasia—introduction
• Section Two: When things go wrong in congenital adrenal hyperplasia
• Section Three: Treatment for congenital adrenal hyperplasia
• Appendix 1: Converting System International (SI) Blood Measures Into North American Values or Conventional Units
• Appendix 2: List of Abbreviations
• Index